And the compound that's left over from this process, an acid called isovaleric acid, starts to build up.

未分解的部分叫做异戊酸，开始积累下来。

This condition, known as isovaleric acidemia, can cause brain damage, and even death, particularly in young children.

这种情况被称为异茂酸酸血症，这会导致大脑损伤，甚至是死亡，尤其对于小孩子来说更是这样。

Here, patients have a genetic mutation that leads to a deficiency in an enzyme called isovaleric co-enzyme A dehydrogenase.

由于患者基因突变会导致缺乏一种酶，被称为——异戊酸辅酶A脱氢酶。

But while isovaleric acid isn't exactly pleasant to smell outside your body, it can be downright damaging to the inside.

然而这种异戊酸让人很不愉快，它能够彻底的损害身体内部。

It's not exactly clear why, but a build-up of isovaleric acid tends to have the most dramatic effects on the central nervous system.

现在还不清楚原因，但异戊酸的积累往往会对中枢神经系统产生剧烈的影响。

There is, so far, no cure for isovaleric acidemia, but some treatments — like avoiding foods rich in leucine, and taking supplements of other, non-threatening amino acids — can help keep patients safe.

目前没有治疗异戊酸血症的方法，但是一些疗法——比如避免进食白氨酸过多的食物，从其他物质中，比如没有威胁的氨基酸，能够保证患者安全。