Urocanic aciduria
（重定向自Urocanase deficiency）
![](/Images/godic/202502/19/Urocanic_acid.svg3815.png")
![Urocanic aciduria has an autosomal recessive pattern of inheritance.](/Images/godic/202502/19/Autorecessive.svg3815.png")
Urocanic aciduria, also called urocanate hydratase deficiency or urocanase deficiency, is an autosomal recessive metabolic disorder caused by a deficiency of the enzyme urocanase. It is a secondary disorder of histidine metabolism.